Anesth Pain Med.  2008 Apr;3(2):139-144.

An Anesthetic Experience in a Patient with Dandy-Walker Malformation : A case report

• Kim SS
• Kwak S
• Kim YK

Abstract

Dandy-Walker malformation is a rare malformation associated with hypoplasia of vermis, a pseudocystic fourth ventricle, upward displacement of the tentorium and lateral sinuses, and anterioposterior enlargement of the posterior fossa. It is frequently associated with genetic anomalies, as well as brain and systemic malformations. Care for these patients requires careful management. Hydrocephalus is present in most patients and clinical presentation is most often heralded by symptoms and signs of hydrocephalus with focal neurologic findings. Treatment is still controversial, and major anesthetic concerns are control of intracranial pressure and evaluation of accompanying organ anomalies. The prognosis is unpredictable and varies mainly according to degree of vermis hypoplasia. We report successful anesthetic management in a child with Dandy-Walker malformation for extra-ventricular drainage.

Keyword

Dandy-Walker malformation; general anesthesia; hydrocephalus; shunt

MeSH Terms

Anesthesia, General
Brain
Child
Dandy-Walker Syndrome
Displacement (Psychology)
Drainage
Fourth Ventricle
Humans
Hydrocephalus
Intracranial Pressure
Neurologic Manifestations
Prognosis
Transverse Sinuses