J Korean Neurosurg Soc.  2011 Nov;50(5):475-477. 10.3340/jkns.2011.50.5.475.

Dandy-Walker Malformation Associated with Neurocutaneous Melanosis

Affiliations
  • 1Department of Neurosurgery, College of Medicine, Ewha Womans University, Seoul, Korea. shsg@ewha.ac.kr

Abstract

Neurocutaneous melanosis associated with Dandy-Walker malformation is a rare dysmorphogenesis that is associated with single or multiple giant pigmented cutaneous nevi and diffuse involvement of the central nervous system. In this article, we present a 2-month-old patient with neurocutaneous melanosis associated with Dandy-Walker malformation. In addition, we reviewed the literature and discussed the pathogenesis based on the preferred hypotheses.

Keyword

Dandy-Walker malformation; Neurocutaneous melanosis; Hydrocephalus

MeSH Terms

Central Nervous System
Dandy-Walker Syndrome
Humans
Hydrocephalus
Infant
Melanosis
Neurocutaneous Syndromes
Nevus
Melanosis
Neurocutaneous Syndromes
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