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J Korean Diabetes Assoc.  2006 Nov;30(6):487-491.

Acquired Generalized Lipodystrophy with Severe Insulin Resistant Diabetes Mellitus

Affiliations
  • 1Department of Internal Medicine, Division of Endocrinology and Metabolism, The Catholic University of Korea, Korea.

Abstract

Acquired generalized lipodystrophy is a rare disease, and often follows autoimmune disease, prodromal infection, HIV infection. The clinical characteristics are generalized absence of fat, insulin resistance, diabetes mellitus, absence of ketosis, elevated basal metabolic rate, severe hypertriglyceridemia, and hepatomegaly. Here we experience and report a case of 16-year-old female patient who has clinical features of acquired generalized lipodystrophy with severe insulin resistant diabetes mellitus without any prodromal states.

Keyword

Diabetes mellitus; Hypertriglyceridemia; Lipodystrophy

MeSH Terms

Adolescent
Autoimmune Diseases
Basal Metabolism
Diabetes Mellitus*
Female
Hepatomegaly
HIV Infections
Humans
Hypertriglyceridemia
Insulin Resistance
Insulin*
Ketosis
Lipodystrophy
Lipodystrophy, Congenital Generalized*
Prodromal Symptoms
Rare Diseases
Insulin
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