Ann Rehabil Med.  2011 Oct;35(5):742-746. 10.5535/arm.2011.35.5.742.

Combined Therapy of Orthopedic Surgery after Deep Brain Stimulation in Cerebral Palsy Mixed Type: A Case Report

• Park HS
• Park ES
• Chang JW
• Lee KS
• Suh YJ
• Cho SR

• KMID: 2267240
• DOI: http://doi.org/10.5535/arm.2011.35.5.742

Abstract

Dystonia is a symptom defined by involuntary and irregular contractions of the muscles, which cause movement disorders and postural problems. Deep brain stimulation (DBS) in globus pallidus interna (GPi) is a good option for controlling dystonia. DBS has already been shown to have significant effects on primary dystonia as well as Parkinson's disease. Dystonia is very difficult to manage, as seen in cerebral palsy (CP) mixed with spasticity. As CP patients grow, their musculoskeletal problems may require orthopedic surgery. However, the outcome of orthopedic surgery is not usually suitable due to dystonia. Therefore, we attempted to control dystonia through DBS initially and perform orthopedic surgery to correct musculoskeletal deformities after treatment of dystonia. Herein, we report a case that showed remarkable improvement in terms of the dystonia rating scale and gait pattern after combined therapy of DBS and orthopedic surgery.

Keyword

Dystonia; Deep brain stimulation; Cerebral palsy

MeSH Terms

Cerebral Palsy
Congenital Abnormalities
Contracts
Deep Brain Stimulation
Dystonia
Dystonic Disorders
Gait
Globus Pallidus
Humans
Movement Disorders
Muscle Spasticity
Muscles
Orthopedics
Parkinson Disease

Figure

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  Fig. 1 Kinematic Changes in Gait Analysis after Combined Therapy of DBS and Orthopedic Surgery. When compared with preoperative state (A), pelvic bump sign, asymmetry of pelvic obliquity and ankle plantar flexion deformity were attenuated after orthopedic surgery performed 6 months after treatment of dystonia with DBS (B). DBS: Deep brain stimulation.

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