Pancreatoblastoma 1 case

Wang, Young Gwon; Kim, Hae Young; Bae, Young Tae; Sim, Mun Sup

Abstract

Pancreatoblastoma is a rarely occurring malignant tumor in childhood, which has been reported less 60cases in the world. which is a kind of adenocarcinoma exhibiting solid encapsulating tumor. Its prognosis is better favorable than typical pancreatic cancer. We were experienced one case of pancreatoblastoma, the patient was a 8 years-old boy who was incidentally found by his parent because of left upper quadrant mass during having a bath without any previous medical history. His preoperative AFP level was elevated and his preoperative diagnosis was pancreatoblastoma by abdominal computed tomography. During laparotomy, the tumor was located between body and tail of pancreas, adhered to hilum of spleen and also surrounded by transverse mesocolon, displacing the arcade of mesocolic vessels. When dissecting the mesocolon from pancreatic tumor, superior mesenteric artery and gastroduodenal artery were embeded in the tumor. The patient underwent distal pancreatectomy and splenectomy after ligature and dividing of mid-colic vessel. After surgery, he was received six-cycle of combined chemotherapy. There is no evidence of recurrence and metastasis for nineteen months after surgery.