J Korean Surg Soc.  2009 Dec;77(Suppl):S29-S32. 10.4174/jkss.2009.77.Suppl.S29.

Pancreatoblastoma in Children

• Park J

• KMID: 1464799
• DOI: http://doi.org/10.4174/jkss.2009.77.Suppl.S29

Abstract

Pancreatoblastoma is a rare pediatric neoplasm with distinct acinar and squamoid differentiation that generally affects infants and young children. Although the prognosis is relatively favorable over typical pancreatic cancer, the optimal treatment of pancreatoblastoma has not been established. We experienced two cases of pancreatoblastoma in a 2-year-old girl and boy which was found incidentally by the parents due to the detection of abdominal masses.

Keyword

Pancreatoblastoma; Children

MeSH Terms

Child
Humans
Infant
Pancreatic Neoplasms
Parents
Preschool Child
Prognosis
Pancreatic Neoplasms

Figure

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  Fig. 1 Contrast enhanced abdominal computed tomography (CT) scan shows well-demarcated, inhomogenous mass with some calcification in head of pancreas.

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  Fig. 2 Cut surface of tumor shows yellowish area intermixing with myxoid area and focal cystic change. Mass is separated by fibrous septa.

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  Fig. 3 Contrast enhanced abdominal CT scan shows well-defined solid mass, which is multilobulated by enhancing septa.

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  Fig. 4 Operative finding shows huge mass originating from tail of pancreas.

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  Fig. 5 Histological examination shows a distinct organoid pattern containing globular structures with elongated cells (Squamoid corpuscles: black arrow) and acinar cells (H&E stain, ×400).

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