Korean J Pediatr.
2006 Feb;49(2):212-216. 10.3345/kjp.2006.49.2.212.
A case of congenital neurocutaneous melanosis
- Affiliations
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- 1Department of Pediatrics, Sung-Ae General Hospital, Seoul, Korea. eunicu@hanmail.net
- 2Department of Radiology, Sung-Ae General Hospital, Seoul, Korea.
- 3Department of Dermatology, Sung-Ae General Hospital, Seoul, Korea.
- KMID: 1966617
- DOI: http://doi.org/10.3345/kjp.2006.49.2.212
Abstract
- Neurocutaneous melanosis is a rare congenital syndrome characterized by the presence of large or multiple congenital melanocytic nevi and benign pigment cell tumors of the leptomeninges. Neurocutaneous melanosis is thought to represent an error in the morphogenesis of embryonal neuroectoderm. We experienced a neonate who presented with giant, dark colored pigmented nevi covering chest, abdomen, neck and arms, with satellite lesions. Magnetic resonance image showed a nodular hyperintense lesion in the amygdala of the right temporal lobe, and T1-weighted images showed hyperintensities in the adjacent leptomeninges. We report a rare case of neurocutaneous melanosis with a brief review of related literature.
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