Korean J Thorac Cardiovasc Surg.  1997 Feb;30(2):205-208.

Successful Removal of Left Ventricular Rhabdomyoma : A Rare Cause of Left Ventricular Outflow Obstruction in the Newborn Infant: 1 case report

• Ahn BH
• Moon HS
• Na KJ
• Kim SH
• Kim BJ
• Ma JS

Abstract

Cardiac rhabdomyomas are the most common primary tumor in infancy and childhood and are frequently associated with tuberous sclerosis. Although spontaneous regression of cardiac rhabdomyoma has been reported , prognosis of this tumor associated with subaortic stenosis is still considered to be poor and surgery continues to be indicated. A 4-day-old female was admitted due to tachypnea and cyanosis. Single rhabdomyoma arising from the interventricular septum associated with severe subaortic stenosis was partially removed under cardiopulmonary bypass. Excised tumor size was 0.7 X 0.9 X 0.4 cm in dimension. The postoperative course was uneventful and the infant discharged on the 14th postoperative day.

Keyword

Ventricular outflow tract obstruction, left; Heart neoplasm; Infant; Rhabdomyoma; Echocardiography

MeSH Terms

Cardiopulmonary Bypass
Constriction, Pathologic
Cyanosis
Echocardiography
Female
Heart Neoplasms
Humans
Infant
Infant, Newborn*
Prognosis
Rhabdomyoma*
Tachypnea
Tuberous Sclerosis
Ventricular Outflow Obstruction*