Korean J Thorac Cardiovasc Surg.  1999 Nov;32(11):1004-1008.

Repair of Total Anomalous Pulmonary Venous Return in Infant

• Hong YS
• Park YH
• Lim SH
• Cho BK
• Rho HK

Abstract

BACKGROUND: Total anomalous pulmonary venous return is a relatively rare disease which has a very high mortality(80% within a year) if not properly corrected surgically. MATERIAL AND METHOD: Twenty-six infants with total anomalous pulmonary venous return underwent repair between May, 1991 and February, 1996. RESULT: There were 19 boys and 7 girls. The mean age at operation was 2.6 months(range: 5 day to 11 month) and the mean body weight was 4.3kg(range:2.8 to 6.7 kg). Preoperative stabilization included ventilator for 5 patients and inotropic support for 6 patients. There were 6 hospital mortalities. Significant risk factors of operative mortality were preoperative ventilator care(p<0.03) and preoperative inotropic support(p<0.05). Age, body weight at operation, pulmonary venous obstruction, high pulmonary arterial pressure, spurasystemic right ventricular pressure or emergency operation did not affected the operative outcome. Postperative pulmonary venous obstruction occurred in three patients 2 or 3 months later, among them one patient was reoperated. The actuarial survival was 76% at 40 months.
CONCLUSION
Although early mortality was high, repair of total anomalous pulmonary venous return should be attempted in early life, but the patients receiving ventilator care or inotropic support need special attention.

Keyword

Pulmonary vein, total anomalous return; Infant

MeSH Terms

Arterial Pressure
Body Weight
Emergencies
Female
Hospital Mortality
Humans
Infant*
Mortality
Rare Diseases
Risk Factors
Scimitar Syndrome*
Ventilators, Mechanical
Ventricular Pressure