Korean J Obstet Gynecol.  2012 Dec;55(12):978-981. 10.5468/KJOG.2012.55.12.978.

A case of prenatal diagnosis of congenital thoracic kidney in the third trimester with congenital diaphragmatic hernia

Affiliations
  • 1Department of Obstetrics and Gynecology, Inje University Haeundae Paik Hospital, Inje University College of Medicine, Busan, Korea. chohj@paik.ac.kr
  • 2Department of Pediatric Surgery, Inje University Haeundae Paik Hospital, Inje University College of Medicine, Busan, Korea.

Abstract

Congenital thoracic kidney is a rare congenital malformation, caused by renal malpositioning during embryogenesis or congenital diaphregmatic hernia with herniation of kidney. Prenatal diagnosis of congenital thoracic kidney has been only rarely reported, underlying congenital diaphragmatic hernia should always be suspected in cases of congenital thoracic kidney. We present a case in which the prenatal diagnosis of an ectopic intrathoracic kidney was made on routine anatomical survey at 29 weeks' gestation.

Keyword

Fetal ultasound; Intrathoracic kidney; Prenatal diagnosis

MeSH Terms

Embryonic Development
Female
Hernia
Hernia, Diaphragmatic
Humans
Kidney
Pregnancy
Pregnancy Trimester, Third
Prenatal Diagnosis
Hernia, Diaphragmatic

Figure

  • Fig. 1 Transverse sonograms of the fetal thorax on prenatal sonographic examination at 29 weeks demonstrate the ectopic kidney (K) in the left hemithorax, compressed left lung (L), mild right shift of the heart (H).

  • Fig. 2 Coronal sonographic view of the fetus. Color Doppler imaging demonstrates the left renal artery entering the thorax to feed the ectopic intrathoracic kidney (white arrow), and normal right renal artery entering the right kidney (hollowed arrow).

  • Fig. 3 Intrathoracic kidney with congenital diaphragmatic hernia on postnatal X-ray (white arrows).

  • Fig. 4 Left thoracic kidney on thoracoscopy (white arrows). D, diaphragm; L, left lung; K, left kidney.


Reference

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