Korean J Hepatol.  2000 Jun;6(2):223-228.

Primary Biliary Cirrhosis Associated with Multiple Renal Abscess and IgA Nephropathy: A Case Report

• Shin JW
• Song IH
• Ki MJ
• Lim CY
• Cho JT

Abstract

Primary biliary cirrhosis is a chronic progressive disease most often affecting women. It is characterized by the progressive destruction of the small intrahepatic bile ducts with portal inflammation leading to hepatic fibrosis and cirrhosis. Autoimmune diseases such as Sjogren's syndrome, rheumatoid arthritis, dermatomyositis, CREST syndrome, and autoimmune thyroiditis may be found in up to 80% of the patients. Primary biliary cirrhosis is also associated with renal diseases such as distal renal tubular acidosis, bacteriuria and glomerulopathy, but there is no case report of primary biliary cirhosis with renal manifestations in Korea. We are reporting a case of primary biliary cirrhosis with multiple renal abscess and IgA nephropathy with a review of the literature.

Keyword

Primary biliary cirrhosis; IgA nephropathy; Renal abscess

MeSH Terms

Abscess*
Acidosis, Renal Tubular
Arthritis, Rheumatoid
Autoimmune Diseases
Bacteriuria
Bile Ducts, Intrahepatic
CREST Syndrome
Dermatomyositis
Female
Fibrosis
Glomerulonephritis, IGA*
Humans
Immunoglobulin A*
Inflammation
Korea
Liver Cirrhosis, Biliary*
Sjogren's Syndrome
Thyroiditis, Autoimmune
Immunoglobulin A