Korean Circ J.  2015 Sep;45(5):439-441. 10.4070/kcj.2015.45.5.439.

Noncompaction of Ventricular Myocardium Involving the Right Ventricle

• Saglam M
• Saygin H
• Kozan H
• Ozturk E
• Mutlu H

• KMID: 2223810
• DOI: http://doi.org/10.4070/kcj.2015.45.5.439

Abstract

Noncompaction ventricular myocardium is an unusual cause of cardiomyopathy. It is association with congenital heart defects, most often with outflow obstructive lesions or coronary anomalies. However, no factor could explain the arrest of development of myocardial structure (isolated form). The pathogenesis of isolated noncompaction is thought to be an arrest in endomyocardial morphogenesis. It has been reported that myocardial noncompaction could present as acquired disease. The most common site of involvement is the left ventricle, with right ventricular involvement being reported in a few cases. In this report, we present a case with noncompaction of the right ventricle (RV). Cardiac computed tomography angiography and magnetic resonance imaging demonstrated morphological abnormalities of the RV.

Keyword

Multidetector computed tomography; Magnetic resonance imaging; Isolated noncompaction of the ventricular myocardium

MeSH Terms

Angiography
Cardiomyopathies
Heart Defects, Congenital
Heart Ventricles*
Isolated Noncompaction of the Ventricular Myocardium
Magnetic Resonance Imaging
Morphogenesis
Multidetector Computed Tomography
Myocardium*

Figure

• 

  Fig. 1 A 72-year old male with noncompaction of right ventricle. A: short axis view of the ventricles on computed tomography imaging showing deep intertrabecular recesses within the right ventricle with a noncompacted to compacted myocardium ratio of 8.5. B: true fast imaging with steady-state precession (true-FISP) cine four-chamber magnetic resonance image delineating noncompaction in the apical region of the right ventricle (star).

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