Yonsei Med J.  2007 Dec;48(6):1052-1055. 10.3349/ymj.2007.48.6.1052.

A Case of Noncompaction of the Ventricular Myocardium Combined with Situs Ambiguous with Polysplenia

Affiliations
  • 1Division of Cardiology Yongdong Severance Hospital, Yonsei University College of Medicine, Seoul, Korea. sejoong@yuhs.ac
  • 2Division of Radiology, Yongdong Severance Hospital, Yonsei University College of Medicine, Seoul, Korea.

Abstract

A 33-year-old man was admitted to our hospital with chest pain and exertional dyspnea. Two-dimensional echocardiography showed prominent trabeculations and deep intertrabecular recesses, findings consistent with noncompaction of the ventricular myocardium. Thoracoabdominal CT and cardiac magnetic resonance imaging (CMR) revealed situs ambiguous with polysplenia and noncompaction of the left ventricular myocardium. CMR also demonstrated delayed enhancement of the trabeculations located at the apical portion of the left ventricle. The coronary angiogram was normal. This is the first case of noncompaction of the ventricular myocardium associated with situs ambiguous with polysplenia.

Keyword

Noncompaction of the ventricular myocardium (NVM); situs ambiguous with polysplenia

MeSH Terms

Abnormalities, Multiple/*pathology
Adult
Echocardiography
Heart Ventricles/abnormalities
Humans
Magnetic Resonance Imaging
Male
Myocardium/*pathology
Spleen/*abnormalities
Syndrome
Tomography, X-Ray Computed
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