J Korean Neurosurg Soc.  2015 Jun;57(6):436-439. 10.3340/jkns.2015.57.6.436.

Posterior Cerebral Artery Insufficiency in Pediatric Moyamoya Disease

• Lee JY
• Kim SK
• Phi JH
• Wang KC

• KMID: 2191251
• DOI: http://doi.org/10.3340/jkns.2015.57.6.436

Abstract

The majority of clinical studies on moyamoya disease (MMD) have focused on anterior circulation. The disease involvement of posterior circulation in MMD, mainly in the posterior cerebral artery (PCA), has been mentioned since the early 1980s, and it has been repeatedly emphasized as one of the most important factors related to poor prognosis in MMD. However, its clinical features and outcome have only been elucidated during the last few years. In this review, the angiographic definition of PCA stenosis is summarized. The clinical features are elucidated as being either early-onset or delayed-onset, according to the time of PCA stenosis diagnosis in reference to the anterior circulation revascularization surgeries. The surgical strategy and hypothesis on the mechanism of PCA stenosis is also briefly mentioned. It appears that some MMD patients may show PCA stenosis during the early or late course of the disease and that the presenting symptoms may vary. Because the hemodynamic compromise caused by PCA stenosis may respond well to surgical treatment, clinicians should be aware of the condition, especially during follow-up of MMD patients.

Keyword

Moyamoya disease; Posterior cerebral artery; Posterior circulation

MeSH Terms

Constriction, Pathologic
Diagnosis
Follow-Up Studies
Hemodynamics
Humans
Moyamoya Disease*
Passive Cutaneous Anaphylaxis
Posterior Cerebral Artery*
Prognosis

Figure

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  Fig. 1 The angle between basilar artery and P1 segment of PCA. PCA : posterior cerebral artery.

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