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J Korean Soc Radiol.  2014 Jun;70(6):435-438. 10.3348/jksr.2014.70.6.435.

CT and MR Imaging Findings of Perianal Dermatofibrosarcoma Protuberans Mimicking Mucinous Adenocarcinoma Arising from Fistula in Ano: A Case Report

Affiliations
  • 1Department of Radiology, Uijeongbu St. Mary's Hospital, College of Medicine, The Catholic University of Korea, Uijeongbu, Korea. ymiku@catholic.ac.kr
  • 2Department of Pathology, Uijeongbu St. Mary's Hospital, College of Medicine, The Catholic University of Korea, Uijeongbu, Korea.
  • 3Department of Surgery, Uijeongbu St. Mary's Hospital, College of Medicine, The Catholic University of Korea, Uijeongbu, Korea.

Abstract

Dermatofibrosarcoma protuberans (DFSP) is an uncommon soft tissue neoplasm which typically originates in the dermis and spreads into the subcutaneous layer and muscle. We report an extremely rare case of a perianal DFSP mimicking mucinous adenocarcinoma arising from anorectal fistula in a 59-year-old woman. In case of a perianal mass, which is connected by a stalk to the anus and shows heterogeneous enhancement without related regional lymphadenopathy, DFSP should be included in the differential diagnosis.


MeSH Terms

Adenocarcinoma, Mucinous*
Anal Canal
Dermatofibrosarcoma*
Dermis
Diagnosis, Differential
Female
Fistula*
Humans
Lymphatic Diseases
Magnetic Resonance Imaging*
Middle Aged
Soft Tissue Neoplasms
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