Korean J Gastrointest Endosc.  2004 May;28(5):251-256.

Ovarian Cystadenofibroma in a Patient with Familial Adenomatous Polyposis

Affiliations
  • 1Department of Internal Medicine, Institute of Gastroenterology, Yonsei University College of Medicine, Seoul, Korea. leesj@yumc.yonsei.ac.kr
  • 2Department of Surgery, Yonsei University College of Medicine, Seoul, Korea.
  • 3Department of Pathology, Yonsei University College of Medicine, Seoul, Korea.

Abstract

Familial adenomatous polyposis (FAP) is a hereditary disease characterized by the appearance of numerous polyps in the large bowel with a high potential for malignant transformation unless untreated. A variety of extracolonic manifestations were reported such as osteoma, epidermoid cyst, desmoid tumor, gastroduodenal polyps, small bowel tumor, congenital hypertrophy of the retinal pigment epithelium, hepatobiliary tumor, thyroid tumor, and tumor of the central nervous system. However, the ovarian involvement of FAP as an extracolonic manifestation was very rare and there have been only few reports. We experienced a rare case of ovarian cystadenofibroma in a patient with FAP as an extracolonic manifestation. We also found colon cancer with multiple hepatic metastasis initially manifested as intestinal obstruction in the same patient. Surgical treatment and subsequent chemotherapy for colon cancer and intraoperative radiofrequency ablation of hepatic metastasis were performed.

Keyword

Familial adenomatous polyposis; Cystadenofibroma; Colon cancer

MeSH Terms

Adenomatous Polyposis Coli*
Catheter Ablation
Central Nervous System
Colonic Neoplasms
Cystadenofibroma*
Drug Therapy
Epidermal Cyst
Fibromatosis, Aggressive
Genetic Diseases, Inborn
Humans
Hypertrophy
Intestinal Obstruction
Neoplasm Metastasis
Osteoma
Polyps
Retinal Pigment Epithelium
Thyroid Gland
Full Text Links
  • KJGE
Actions
Cited
CITED
export Copy
Close
Share
  • Twitter
  • Facebook
Similar articles
Copyright © 2024 by Korean Association of Medical Journal Editors. All rights reserved.     E-mail: koreamed@kamje.or.kr