Soonchunhyang Med Sci.  2014 Dec;20(2):140-144. 10.0000/sms.2014.20.2.140.

A Case of Egg-Shell Calcification of Renal Cell Carcinoma in Continuous Ambulatory Peritoneal Dialysis Patient with Sclerosing Encasulating Peritonitis

• Lee SN
• Kim SI
• Han JY
• Song JH
• Lee SW
• Kim MJ

• KMID: 2317742
• DOI: http://doi.org/10.0000/sms.2014.20.2.140

Abstract

Acquired cystic kidney disease (ACKD), a common complication in patients with end-stage renal disease, is characterized by more than three kidney cysts and normal or decreased sizes of both kidneys without any familial history of cystic kidney disease. In autosomal dominant polycystic kidney disease (ADPKD), however, both kidneys are usually enlarged. Extrarenal manifestations are common in ADPKD, including hepatic cysts, seminal vesicle cysts, mitral valve prolapse. A 40-year-old man presented to the emergency clinic at Inha University Hospital with severe abdominal pain, nausea, and vomiting for 3 days. He had been undergoing continuous ambulatory peritoneal dialysis (CAPD) for 15 years, but it was recently changed to hemodialysis owing to sclerosing encapsulating peritonitis (SEP). Radiologic imaging studies revealed bilateral enlarged kidneys with multiple eggshell calcified cysts and some hepatic cysts, which suggested ADPKD. He underwent left nephrectomy, and pathological tests revealed ACKD-associated renal cell carcinoma (RCC) confined to the resected kidney. He was treated with steroids for SEP, and the symptoms resolved. We herein report a case of ACKD-resembling ADPKD-that progressed to RCC in a patient with concurrent SEP who had been undergoing CAPD for 15 years.

Keyword

Kidney disease, cystic; Polycystic kidney, autosomal dominant; Carcinoma, renal cell; Renal insufficiency, chronic; Peritoneal dialysis, continuous ambulatory

MeSH Terms

Abdominal Pain
Adult
Carcinoma, Renal Cell*
Emergencies
Humans
Kidney
Kidney Diseases, Cystic
Kidney Failure, Chronic
Mitral Valve Prolapse
Nausea
Nephrectomy
Peritoneal Dialysis, Continuous Ambulatory*
Peritonitis*
Polycystic Kidney, Autosomal Dominant
Renal Dialysis
Renal Insufficiency, Chronic
Seminal Vesicles
Steroids
Vomiting
Steroids