Korean J Obstet Gynecol.  2012 Sep;55(9):673-677. 10.5468/KJOG.2012.55.9.673.

A case of primary ovarian low-grade endometrial stromal sarcoma

• Yi WH
• Shin KS
• Je GH
• Lee HS
• Baik KD

• KMID: 2274142
• DOI: http://doi.org/10.5468/KJOG.2012.55.9.673

Abstract

Endometrial stromal sarcoma (ESS) is a relatively rare form of uterine sarcoma. ESS of the myometrium compose just 0.2% of uterine malignant tumors. Low-grade ESS has extended beyond the uterus in 40% of cases at the time of diagnosis. ESS of ovary is very rare. Most of ovarian ESS is concomitant with endometriosis or same tumor in uterus. We have experienced a primary ovarian low-grade ESS, and that sarcoma is localized in ovary. So, we report this case with review of literature.

Keyword

Sarcoma, endometrial stromal, low grade; Ovarian neoplasms

MeSH Terms

Animals
Endometriosis
Female
Mice
Myometrium
Ovarian Neoplasms
Ovary
Sarcoma
Sarcoma, Endometrial Stromal
Uterus

Figure

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  Fig. 1 Abdominal computed tomography (CT). Coronal (A) and horizontal (B) CT showing mixed density 11.6×9.2 cm solid mass (arrow) in pelvic cavity, abutting uterus with poor enhancements.

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  Fig. 2 Transvaginal ultrasonography shows mixed echogenic solid mass in pelvic cavity.

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  Fig. 3 Dense cellular neoplasm, composed of ovoid cells with interspersed small arterioles (H&E, ×40).

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  Fig. 4 The ovoid tumor cells are arranged concentrically around the spiral arterioles (H&E, ×200).

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  Fig. 5 Interstitial hemorrhage and congestion, due to torsion (H&E, ×200).

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