Korean J Med.  2014 May;86(5):632-636.

A Case of Primary Autoimmune Myelofibrosis

Affiliations
  • 1Department of Internal Medicine, School of Medicine, CHA University, Seongnam, Korea. doh@cha.ac.kr
  • 2Department of Pathology, School of Medicine, CHA University, Seongnam, Korea.

Abstract

Primary autoimmune myelofibrosis, the development of which is not preceded by a well-defined autoimmune disease, has recently been defined as a distinct clinicopathologic syndrome. We report herein a case of a 68-year-old woman who was diagnosed with primary autoimmune myelofibrosis and present a review of the literature. The patient manifested peripheral pancytopenia, was positive for autoantibodies, and developed myelofibrosis with no preceding autoimmune or hematologic disorders. Her condition was dramatically improved after administration of prednisolone.

Keyword

Primary autoimmune myelofibrosis; Leukoerythroblastosis; Prednisolone

MeSH Terms

Aged
Autoantibodies
Autoimmune Diseases
Female
Humans
Pancytopenia
Prednisolone
Primary Myelofibrosis*
Autoantibodies
Prednisolone
Full Text Links
  • KJM
Actions
Cited
CITED
export Copy
Close
Share
  • Twitter
  • Facebook
Similar articles
Copyright © 2024 by Korean Association of Medical Journal Editors. All rights reserved.     E-mail: koreamed@kamje.or.kr