Korean J Med.  2015 Dec;89(6):738-741. 10.3904/kjm.2015.89.6.738.

Churg-Strauss Syndrome Presenting with Diffuse Alveolar Hemorrhage

Affiliations
  • 1Department of Internal Medicine, Chonbuk National University Medical School and Research Institute of Clinical Medicine of Chonbuk National University Hospital, Jeonju, Korea.
  • 2Division of Rheumatology, Department of Internal Medicine, Chonbuk National University Medical School and Research Institute of Clinical Medicine of Chonbuk National University Hospital, Jeonju, Korea. ywhim@jbnu.ac.kr

Abstract

Churg-Strauss syndrome (CSS), known as eosinophilic granulomatosis with polyangiitis, is a rare type of systemic vasculitis characterized by the presence of asthma, peripheral eosinophilia, and necrotizing vasculitis with eosinophilic infiltration of multiple organs. Approximately 3-4% of all CSS cases are associated with alveolar hemorrhage. Untreated CSS may lead to a poor prognosis, but glucocorticoid and cytotoxic agent treatments may result in clinical remission. The careful diagnosis and understanding of CSS is important for making treatment decisions and providing effective care. Here, we report a case of CSS with diffuse alveolar hemorrhage.

Keyword

Churg-Strauss syndrome

MeSH Terms

Asthma
Churg-Strauss Syndrome*
Diagnosis
Eosinophilia
Eosinophils
Hemorrhage*
Prognosis
Systemic Vasculitis
Vasculitis
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