Korean J Nephrol.  2007 Nov;26(6):779-783.

Coexistence of the Renal Fibromuscular Dysplasia and Familial Adenomatous Polyposis

Affiliations
  • 1Department of Internal Medicine, Wonkwang University School of Medicine, Iksan, Korea. yumin0525@hanmail.net
  • 2Department of Pathology, Wonkwang University School of Medicine, Iksan, Korea.

Abstract

Fibromuscular dysplasia (FMD) is a nonatherosclerotic, noninflammatory vascular disease that most commonly affects the renal and internal carotid arteries. A Familial adenomatous polyposis (FAP) is characterized by hundreds of adenomatous colorectal polyps, with an almost inevitable progression to colorectal cancer. A 19-year-old woman with history of total colectomy as a result of familial adenomatous polyposis presented with high blood pressure incidentally. Abdominal CT scan showed "string of beads" appearance of right renal artery. Percutaneous transluminal renal angioplasty was performed and then hypertension was improved. To our knowledge, there has been no previous case report of secondary renovascular hypertension resulting from fibromuscular dysplasia in patients with FAP. Here, we report a patient with a review of the literature.

Keyword

Fibromuscular dysplasia (FMD); Familial adenomatous polyposis (FAP); Renovascular hypertension

MeSH Terms

Adenomatous Polyposis Coli*
Angioplasty
Carotid Artery, Internal
Colectomy
Colorectal Neoplasms
Female
Fibromuscular Dysplasia*
Humans
Hypertension
Hypertension, Renovascular
Polyps
Renal Artery
Tomography, X-Ray Computed
Vascular Diseases
Young Adult
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