J Rheum Dis.  2011 Dec;18(4):292-296. 10.4078/jrd.2011.18.4.292.

A Case of Henoch-Schonlein Purpura Complicated by Acute Pancreatitis and Interstitial Pneumonitis

Affiliations
  • 1Division of Rheumatology, Division of Gastroenterology, Department of Internal Medicine, Busan Medical Center, Busan, Korea. jiny0122a@daum.net
  • 2Department of Pathology, Busan Medical Center, Busan, Korea.

Abstract

Henoch-Schonlein purpura (HSP) is a systemic vasculitis involving the skin, gut, joint and kidney that is characterized by immunoglobulin A (IgA)-dominant immune deposits in target organs. Gastrointestinal involvement is known to be relatively common, but acute pancreatitis and pulmonary involvement are rare in Henoch-Schonlein purpura. We experienced a case of a 46-year-old man who developed adult-onset HSP complicated by acute pancreatitis and interstitial pneumonitis. The patient received corticosteroid therapy at a dosage of 0.5 mg/kg. After corticosteroid therapy, patient's symptoms improved. We report here the first case of HSP complicated by acute pancreatitis and interstitial pneumonitis.

Keyword

Henoch-Schonlein purpura; Pancreatitis; Pneumonitis

MeSH Terms

Humans
Immunoglobulin A
Joints
Kidney
Lung Diseases, Interstitial
Middle Aged
Pancreatitis
Pneumonia
Purpura, Schoenlein-Henoch
Skin
Systemic Vasculitis
Immunoglobulin A
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