J Korean Ophthalmol Soc.  2009 Jun;50(6):946-950. 10.3341/jkos.2009.50.6.946.

A Case of Melanocytoma of the Ciliary Body

• Choi SW
• Seo SG
• Her J

• KMID: 2212376
• DOI: http://doi.org/10.3341/jkos.2009.50.6.946

Abstract

PURPOSE: To report a patient with melanocytoma of the ciliary body.
METHODS
A 52-year-old woman, who transferred from a private ophthalmic clinic to our hospital after a cataract operation due to a mass behind the iris, was evaluated. The patient had a dark brown mass with a smooth surface confirmed by ultrasonogram, CT, and MRI. The mass was removed by en bloc resection.
RESULTS
The tumor had a gross finding of a dark brown, soft, and smooth surface 0.5x0.5x0.5 cm in size. Histopathologic examination revealed a melanocytoma originating in the ciliary body. There was no evidence of metastasis.
CONCLUSIONS
A very rare ciliary body melanocytoma was discovered with a good surgical result obtained by its removal.

Keyword

Ciliary body; Malignant melanoma; Melanocytoma

MeSH Terms

Cataract
Ciliary Body
Female
Humans
Iris
Melanoma
Middle Aged
Neoplasm Metastasis

Figure

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  Figure 1. Preoperative slit lamp examination of melanocytoma of the ciliary body showing at 11 o'clock position along dilated pupil margin.

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  Figure 2. Preoperative orbit CT finding: tumorous lesion at inferolateral aspect of the iris or ciliary body in the right eyeball.

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  Figure 3. Preoperative orbit MRI finding: well-defined, round mass with signal alteration and intense enhancement at the inferolateral aspect of the right iris or ciliary body.

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  Figure 4. Gross finding of excised tumor mass, which is dark brown, soft, and smooth surfaced and 0.5×0.5 ×0.5 cm in size.

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  Figure 5. Microscopic appearance of melanocytoma of the ciliary body (A) (Histopathologic examination, ×40) tumor cells are polygonal melanocytes with small vesicular nuclei and abundant cytoplasm totally packed with melanin granules (B) tumor cells after bleaching preparation have abundant melanin pigment in the cytoplasm.

Reference

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