J Korean Neurosurg Soc.  1998 May;27(5):667-671.

Foix-Alajouanine Syndrome: Case Report

Affiliations
  • 1Department of Neurosurgery, Samsung Medical Center, College of Medicine, Sung Kyun Kwan University, Seoul, Korea.

Abstract

Acute or subacute myelopathy with spontaneous thrombosis of the veins in a patient with a spinal arteriovenous malformation(AVM) has been referred to as "Foix-Alajouanine syndrome(FAS)". A previously healthy 15-year-old girl developed neurological illness with progressive lower extremity weakness and low back pain. The MRI demonstrated the diffuse swelling of the spinal cord around the 10th thoracic level, suggesting myelopathy. Her neurological symptoms deteriorated to paraplegia, voiding difficulty and areflexia. Spinal arteriography did not demonstrate a vascular lesions such as arteriovenous malformation(AVM) or arteriovenous fistula(AVF). Operation revealed diffuse necrosis of the spinal cord and one abnormal thrombosed drainage vein. Progressive clinical illness, the histopathology of the patchy necrosis of spinal cord tissue and many thickened blood vessels are compatible with Foix-Alajouanine syndrome. We report a case of Foix-Alajouanine syndrome with a review of the literature.

Keyword

Foix-Alajouanine syndrome; Arteriovenous malformation; Arteriovenous fistula

MeSH Terms

Adolescent
Angiography
Arteriovenous Fistula
Arteriovenous Malformations
Blood Vessels
Drainage
Female
Humans
Low Back Pain
Lower Extremity
Magnetic Resonance Imaging
Necrosis
Paraplegia
Spinal Cord
Spinal Cord Diseases
Thrombosis
Veins
Full Text Links
  • JKNS
Actions
Cited
CITED
export Copy
Close
Share
  • Twitter
  • Facebook
Similar articles
Copyright © 2024 by Korean Association of Medical Journal Editors. All rights reserved.     E-mail: koreamed@kamje.or.kr