J Korean Neurosurg Soc.  1989 Mar;18(3):486-490.

Atlanto-Axial Dislocation with Spinal Cord Compression in a Mongoloid Child: A Case Report

• Kim SI
• Han YP
• Hong SK
• Hu C
• Kim HJ

Abstract

Mongolism, which represents about 5% to 10% of all cases of mental deficiency, is a disease entity in which the mental development is associated in a unique way with a large number of physical defects including central nervous system. Tishler and Martel(1965) directed attention to anomalies of the cervical portion of the spine in mongologid patients. Ligament laxity or malformation of the transverse atlanta ligament may allow the CI vertebra to subluxate forward with or without spinal cord compression. The most proper management is reduction by skeletal traction and posterior spinal fusion(C1-2, C1-3, Occiput-C2).

Keyword

Mongolism(down syndrome); Physical defects; Ligament laxity; Atlanto-axial dislocation; Spinal cord compression

MeSH Terms

Central Nervous System
Child*
Dislocations*
Down Syndrome
Humans
Intellectual Disability
Ligaments
Spinal Cord Compression*
Spinal Cord*
Spine
Traction