Korean J Thorac Cardiovasc Surg.  2002 Sep;35(9):692-696.

Pulmonary Artery Sarcoma: One Case Report

• Kim HR
• Kim KH
• Ahn H

Abstract

Pulmonary artery sarcoma is a rare disease and hard to diagnose; therefore, suspicion is very important for the diagnosis and treatment. Surgical resection is almost always needed because of progressive right heart failure. Adjuvant chemotherapy and radiation therapy are still controversial. We report a case of a 42-year-old man who had a right pulmonary arterial tumor. Curative resection was impossible because the tumor invaded the left pulmonary artery. Palliative endarterectomy was performed followed by radiation therapy. The patient refused the chemotherapy. Until the postoperative 6th month, the residual tumor was stable. However, 15 months later, follow-up chest computed tomography revealed a metastatic pulmonary nodule at left lower lobe and the increased residual tumor. The patient received chemotherapy with limited tumor response. The metastatic nodule and residual tumor did not increase but bone scan revealed a rib metastasis at postoperative 24 months. He will be receiving additional chemotherapy.

Keyword

Pulmonary artery; Vascular neoplasm; Sarcoma

MeSH Terms

Adult
Chemotherapy, Adjuvant
Diagnosis
Drug Therapy
Endarterectomy
Follow-Up Studies
Heart Failure
Humans
Neoplasm Metastasis
Neoplasm, Residual
Pulmonary Artery*
Rare Diseases
Ribs
Sarcoma*
Thorax
Vascular Neoplasms