J Korean Neurosurg Soc.  2012 Nov;52(5):488-490. 10.3340/jkns.2012.52.5.488.

A Neuro-Behcet's Case Operated with the Intracranial Mass Misdiagnosis

• Tokgoz OS
• Akpinar Z
• Guney F
• Seyithanoglu A

• KMID: 2018258
• DOI: http://doi.org/10.3340/jkns.2012.52.5.488

Abstract

Behcet's disease (BD) is an inflammatory systemic disorder with oral and genital ulcers, as well as ophthalmologic and cutaneous symptoms. Neurological manifestations in BD represent between 2.2% to 50% of the cases. The 25-year-old male patient, diagnosed with BD three years earlier, was admitted to our clinic with complaints of recurrent headaches. Tumor-like-parenchimal involvement was detected on a cranial magnetic resonance imaging. The lesion was removed surgically and then he suffered from right hemiparesis and epilepsy. Pathological examination of the lesion noted a demyelinating non-tumoural etiology. A neuro-Behget's case with parenchymal involvement has been examined in light of the literature, in terms of a tumor and a demyelinating disease differential diagnosis.

Keyword

Neuro-Behcet; Intracranial mass; Multiple skleroz; Behcet's disease

MeSH Terms

Demyelinating Diseases
Diagnosis, Differential
Diagnostic Errors
Epilepsy
Headache
Humans
Light
Magnetic Resonance Imaging
Male
Neurologic Manifestations
Paresis
Ulcer

Figure

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  Fig. 1 Contrast-enhanced lesion, which is thought to be accordant with choroiditis or tumour diameter of 1 cm, on left lateral ventricle posterior horn and near the left temporal lobe uncus.

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  Fig. 2 Postoperative images of intensive oedema areas on left temporo-parietal, left mesencephalic hemisphere and porencephalic area.

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