Korean J Clin Neurophysiol.  2015 Jun;17(1):28-30. 10.14253/kjcn.2015.17.1.28.

A Fatal Case of Full-Blown Neuro-Behcet Disease

• Na BS
• Kwon YN
• Song SJ
• Song JM
• Woo HG
• Lee D
• Ahn TB

• KMID: 2225217
• DOI: http://doi.org/10.14253/kjcn.2015.17.1.28

Abstract

We reported a 48-year-old man with Behcet disease, who presented with right hemiparesis. His first brain MRI showed multiple enhanced lesions. During the recovery, he had an episode of left 6th nerve palsy without new lesions in a follow-up MRI. Third episode was cervical myelitis, resulting in respiratory difficulty and quadriplegia without any reflexes. The myelitis was not responsive to immunotherapy. He died of respiratory failure complicated with pneumonia. This is a rare case of full-blown neuro-Behcet disease.

Keyword

Behcet disease; Neuro-Behcet disease; Brainstem; Spinal cord

MeSH Terms

Abducens Nerve Diseases
Behcet Syndrome
Brain
Brain Stem
Follow-Up Studies
Humans
Immunotherapy
Magnetic Resonance Imaging
Middle Aged
Myelitis
Paresis
Pneumonia
Quadriplegia
Reflex
Respiratory Insufficiency
Spinal Cord

Figure

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  Fig. 1. Brain magnetic resonance imaging (MRI) shows multiple lesions in the left pons and the temporooccipital cortices on gadolinium (Gd)-enhanced T1 weighted images. Tentorium cerebelli are also enhanced by Gd (A). Spine MRI shows high signal intensity on T2 weighted image in the cervical cord (B).

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