Korean J Thorac Cardiovasc Surg.  2003 Jul;36(7):523-526.

Bidirectional Cavopulmonary Shunt for Isolated Right Ventricular Endomyocardial Fibrosis

Affiliations
  • 1Department of Thoracic and Cardiovascular Surgery, Keimyung University, School of Medicine, Korea. nhpark@dsmc.or.kr

Abstract

A 44-year-old man had been admitted for dyspnea on exertion and abdominal distension. The echocardiography revealed abnormal mass in right atrium and tricuspid valve stenosis with right ventricular obliteration. The operation was performed with mass removal, enlargement of tricuspid valve opening, and right ventricular endocardiectomy. And then, atrial septal defect was made due to inadequate right ventricular volume. The patient's symptom was improved and he discharged without events. The endomyocardial fibrosis was diagnosed with microscopic examination. Eighteen months later, the patient was readmitted due to aggravated dyspnea and cyanosis. The right ventricular obliteration was progressed and pulmonary blood flow was severely decreased in follow up echocardiography. Palliative bidirectional cavo-pulmonary shunt was performed due to functional single ventricle. The dyspnea and cyanosis was markedly improved. Bidirectional cavo-pulmonary shunt for advanced and isolated right ventricular endomyocardial fibrosis provided effective palliation at early postoperative period, However, long-term follow up is mandatory.

Keyword

Endomyocardial fibrosis; Bidirectional cavo-pulmonary shunt; Shunt

MeSH Terms

Adult
Cyanosis
Dyspnea
Echocardiography
Endomyocardial Fibrosis*
Follow-Up Studies
Fontan Procedure*
Heart Atria
Heart Septal Defects, Atrial
Humans
Postoperative Period
Tricuspid Valve
Tricuspid Valve Stenosis
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