Korean J Thorac Cardiovasc Surg.  2003 Sep;36(9):683-686.

Isolated Right Ventricular Hypoplasia: A case report

Affiliations
  • 1Department of Thoracic and Cardiovascular Surgery, Chosun University College of Medicine, Gwangju, Korea.
  • 2Department of Thoracic and Cardiovascular Surgery, Sejong General Hospital, Bucheon, Korea. woonghan@korea.com

Abstract

Isolated right ventricular hypoplasia is a rare clinical entity. We describe a case of right ventricular hypoplasia, single atrium and spongy myocardium of left ventricle. The volume of right ventricle was half the volume of left ventricle and z-value of tricuspid valve was -4 preoperatively. The patient, 6-year-old boy, underwent atrial partitioning with 3 mm fenestration. Postoperative course was smooth and he tolerated the biventricular state well during follow-up. Follow-up catherterization was done 27 months later. The tricuspid valve grew well (z-value=-0.4) and atrial septal fenestration is closed spontaneously. This article reports a case of successful biventricular repair in a patient with isolated right ventricular hypoplasia.

Keyword

Hypoplastic right ventricle; Atrium; Congenital heart defect

MeSH Terms

Child
Follow-Up Studies
Heart Defects, Congenital
Heart Ventricles
Humans
Male
Myocardium
Tricuspid Valve
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