Cardiovasc Imaging Asia.  2021 Apr;5(2):51-53. 10.22468/cvia.2021.00066.

Isolated Right Ventricular Apical Hypoplasia: A Case Report with 18 Years of Follow Up

Affiliations
  • 1Departments of Radiology, Mie University Hospital, Tsu, Japan
  • 2Department of Cardiology, Mie Prefectural General Medical Center, Yokkaichi, Japan
  • 3Department of Cardiology and Nephrology, Mie University Graduate School of Medicine, Tsu, Japan

Abstract

Isolated right ventricular (RV) hypoplasia is a rare congenital anomaly in which the apical trabecular component of the ventricle fails to develop. In severe forms of isolated RV hypoplasia, patients usually develop cyanosis early in life and require prompt surgical intervention. Mild forms, however, can be asymptomatic until the development of severe tricuspid regurgitation due to annular dilatation. We report a 50-year-old woman with isolated RV apical hypoplasia who presented to our hospital 18 years ago and was followed with serial imaging studies.

Keyword

Congenital heart disease; Magnetic resonance imaging; X-ray computed tomography
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