Korean J Otolaryngol-Head Neck Surg.  1999 Jul;42(7):927-931.

A Case of Infantile Fibromatosis of Neck

• Kim KM
• Han JW
• Kim HS
• Suh JW

Abstract

Infantile fibromatosis, which represents the childhood counterpart of musculoaponeurotic fibromatosis (abdominal or extraabdominal desmoid), usually arises as a solitary mass in skeletal muscle or in the adjacent fascia, aponeurosis, or periosteum. It chiefly affects children from birth to 8 years of age and is slightly more common in boys than in girls. Although infantile fibromatosis is a benign tumor, its nature is malignant for an aggressive clinical course with a tendency to recur in high percentage. Complete excision with an ample margin, the choice of treatment, is often extremely difficult and in some cases, may be impossible without disfigurement or dysfuction. In recurred cases, supplemental radiotherapy and chemotherapy can be tried. We present one case of infantile fibromatosis that has appeared at the right neck during first several months of life. The lesion was excised and diagnosis was confirmed by histologic examination. Some reviews with literature were supplemented.

Keyword

Fibromatosis; Infantile

MeSH Terms

Child
Diagnosis
Drug Therapy
Fascia
Female
Fibroma*
Humans
Muscle, Skeletal
Neck*
Parturition
Periosteum
Radiotherapy