Korean J Urol.  2012 Oct;53(10):733-736. 10.4111/kju.2012.53.10.733.

Primary Undifferentiated Penile Sarcoma in Adolescence

• Choi YH
• Kim HW
• Ahn JH
• Hwang DS
• Lee JW
• Lee BK
• Jun SE
• Lim YT
• Lee SD
• Ha HK

• KMID: 1856995
• DOI: http://doi.org/10.4111/kju.2012.53.10.733

Abstract

We report a case of primary penile undifferentiated sarcoma. A 16-year-old adolescent man visited Pusan National University Hospital complaining of a painless mass on his penis that was increasing in size. Magnetic resonance images revealed a 5x5-cm mass and pathological examinations revealed small round cell sarcomas with neuroendocrine differentiation. The tumor, which had metastatic pulmonary nodules, was treated by tumorectomy and systemic chemotherapy. Thirty-four months after the initial diagnosis, the patient was still alive without evidence of local recurrence or metastatic disease. This is our second case of an undifferentiated penile sarcoma.

Keyword

Adolescence; Penile cancer; Sarcoma

MeSH Terms

Adolescent
Humans
Magnetic Resonance Spectroscopy
Male
Penile Neoplasms
Penis
Recurrence
Sarcoma

Figure

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  FIG. 1 Magnetic resonance images showing a 5-cm mass lesion on the left side of the penis. The mass invaded the corpus cavernosum and corpus spongiosum. This mass arising from the corpus cavernosum showed heterogeneous high signal intensity on the T2-weighted image.

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  FIG. 2 Gross findings of the penile mass. The hypervascular mass is present on the left side of the penis and had a hard consistency and irregular shape. The mass grossly invaded the corpus cavernosum and spongiosum.

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  FIG. 3 Small round cell sarcomas, type not determined, with neuroendocrine differentiation (H&E, ×400). The tumor was composed of mixed round and oval cells with low mitotic activity (less than 3/10 HPFs) and relative monomorphic cytomorphology.

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