Nucl Med Mol Imaging.
2010 Jun;44(2):150-153.
Bone Scintigraphy Findings of A Case with Maffucci's Syndrome
- Affiliations
-
- 1Department of Nuclear Medicine, Seoul National University College of Medicine, Seoul National University Bundang Hospital, 300 Gumi-dong, Bundang-gu, Seongnam-si, Gyeonggi-do 463-707, Korea. jjwalking@naver.com
- 2Department of Pathology, Seoul National University College Medicine, Seoul National University Bundang Hospital, Seongnam-si, Korea.
Abstract
- Maffucci's syndrome is a sporadic rare congenital disease that is characterized by enchondromatosis and soft tissue hemangiomas. A systemic evaluation should be considered because this syndrome is related to generalized mesodermal dysplasia, which has a high likelihood of a malignant transformation. Whole-body bone scintigraphy might be helpful for detecting skeletal involvement. We present a case of Maffucci's syndrome using bone scintigraphy to evaluate the extent of the disease.
