J Korean Ophthalmol Soc.  2019 Sep;60(9):887-891. 10.3341/jkos.2019.60.9.887.

Sjögren's Reticular Retinal Dystrophy

Affiliations
  • 1Department of Ophthalmology, Samsung Medical Center, Sungkyunkwan University School of Medicine, Seoul, Korea. kangsewoong@gmail.com

Abstract

PURPOSE
To report a rare case of Sjögren's reticular retinal dystrophy.
CASE SUMMARY
A 54-year-old male presented with blurred vision and metamorphopsia in both eyes since a few years prior to his initial visit. There was a bilateral reticular network of yellow deposits throughout the posterior pole on fundus examination, which was hyperautofluorescent in fundus autofluorescence photographs. The pigment alterations were more visible with fluorescein angiography, which showed hypofluorescent lesions with hyperfluorescent borders. Spectral-domain optical coherence tomography showed elevations of the outer retina associated with the presence of subretinal hyperreflective material. Based on the conclusive correlation with clinical features, we diagnosed Sjögren's reticular retinal dystrophy.
CONCLUSIONS
Sjögren's reticular retinal dystrophy is characterized by its specific pigment changes at the level of clinical manifestations and the retinal pigment epithelium. In cases of Sjögren's reticular retinal dystrophy, close monitoring is required because it has a lifetime risk of choroidal neovascularization.

Keyword

Macular dystrophy; Pattern dystrophy

MeSH Terms

Choroidal Neovascularization
Fluorescein Angiography
Humans
Macular Degeneration
Male
Middle Aged
Retina
Retinal Dystrophies*
Retinal Pigment Epithelium
Retinaldehyde*
Tomography, Optical Coherence
Vision Disorders
Retinaldehyde
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