Korean J Gastroenterol.  2016 Feb;67(2):116-118. 10.4166/kjg.2016.67.2.116.

Primary Intestinal Lymphangiectasia Diagnosed by Chylous Ascites

• Kang HR
• Cho YK
• Jo YJ
• Jung YY
• Kim EK

• KMID: 2383552
• DOI: http://doi.org/10.4166/kjg.2016.67.2.116

Abstract

No abstract available.

Figure

• 

  Fig. 1. Contrastenhanced abdomen CT. Nodularity of inner layer with mucosal enhancement of gastric antrum (white arrow), and ascites (black arrow) are seen.

• 

  Fig. 2. Ascites. There are gross milky color fluids obtained by paracentesis.

• 

  Fig. 3. Lymphangiography. There is no abrupt cut off sign or dermal back flow on lymphatic drainage.

• 

  Fig. 4. Enteroscopic findings. (A) Round elevated lesion with whitish paches. (B) After performing biopsies, white lymphatic fluid was seen flowing out from the biopsy site.

• 

  Fig. 5. Microscopic finding. The pathologic finding of proximal jejunal lesion shows dilated lymphatics containing proteinaceous fluid (H&E, ×200).

Reference

References

1. Wen J, Tang Q, Wu J, Wang Y, Cai W. Primary intestinal lymphangiectasia: four case reports and a review of the literature. Dig Dis Sci. 2010; 55:3466–3472.

2. Vignes S, Bellanger J. Primary intestinal lymphangiectasia (Waldmann's disease). Orphanet J Rare Dis. 2008; 3:5.

3. Umar SB, DiBaise JK. Protein-losing enteropathy: case illus-trations and clinical review. Am J Gastroenterol. 2010; 105:43–49.

4. Oh TG, Chung JW, Kim HM, et al. Primary intestinal lymphangiectasia diagnosed by capsule endoscopy and double balloon enteroscopy. World J Gastrointest Endosc. 2011; 3:235–240.

5. Rao R, Shashidhar H. Intestinal lymphangiectasia presenting as abdominal mass. Gastrointest Endosc. 2007; 65:522–523.

6. Maamer AB, Baazaoui J, Zaafouri H, Soualah W, Cherif A. Primary intestinal lymphangiectasia or Waldmann's disease: a rare cause of lower gastrointestinal bleeding. Arab J Gastroenterol. 2012; 13:97–98.

7. Imbesi V, Ciccocioppo R, Corazza GR. Long-standing intestinal lymphangiectasia detected by double-balloon enteroscopy. Clin Gastroenterol Hepatol. 2011; 9:e88–e89.

8. Chamouard P, Nehme-Schuster H, Simler JM, Finck G, Baumann R, Pasquali JL. Videocapsule endoscopy is useful for the diagnosis of intestinal lymphangiectasia. Dig Liver Dis. 2006; 38:699–703.

9. Filik L, Oguz P, Koksal A, Koklu S, Sahin B. A case with intestinal lymphangiectasia successfully treated with slow-release octreotide. Dig Liver Dis. 2004; 36:687–690.

10. Suehiro K, Morikage N, Murakami M, Yamashita O, Hamano K. Late-onset primary intestinal lymphangiectasia successfully managed with octreotide: a case report. Ann Vasc Dis. 2012; 5:96–99.

11. Zhu LH, Cai XJ, Mou YP, Zhu YP, Wang SB, Wu JG. Partial enter-ectomy: treatment for primary intestinal lymphangiectasia in four cases. Chin Med J (Engl). 2010; 123:760–764.