Ann Dermatol.
2017 Jun;29(3):381-382. 10.5021/ad.2017.29.3.381.
Hunter Syndrome with Extensive Mongolian Spots
- Affiliations
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- 1Department of Dermatology, School of Medicine, Pusan National University, Busan, Korea. hcko@pusan.ac.kr
- 2Bio-Medical Research Institute, Pusan National University Hospital, Busan, Korea.
- 3Department of Dermatology, Pusan National University Yangsan Hospital, Yangsan, Korea.
- 4Research Institute for Convergence of Biomedical Science and Technology, Pusan National University Yangsan Hospital, Yangsan, Korea.
- KMID: 2378550
- DOI: http://doi.org/10.5021/ad.2017.29.3.381
Abstract
- No abstract available.
MeSH Terms
Figure
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Fig. 1 (A) Extensive round and oval patches of blue-gray hyperpigmentation on the back. (B, C) Numerous firm, ivory-colored papules with a pebbly appearance on both arms. (D) A coarse face, flattened nasal bridge, and shortened neck.
Fig. 2 A biopsy specimen from an ivory-colored papule showing (A) loosely arranged collagen fibers and (B) mucin accumulation (A: H&E, ×100; B: Alcian blue pH 2.5, ×100) compared to (C, D) normal tissue (C: H&E, ×100; D: Alcian blue pH 2.5, ×100).
Reference
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