J Korean Pediatr Soc.  2002 Oct;45(10):1298-1301.

A Case of Systemic Capillary Leak Syndrome in a Child

• Lee TY
• Chung YM
• Kang HG
• Ha IS
• Cheong HI
• Choi Y

Abstract

Systemic capillary leak syndrome(SCLS) is a rare disorder of unknown etiology, which is characterized by recurrent attacks of hypotension, hemoconcentration, and hypoalbuminemia. Urinary or enteric loss of protein is not demonstrated. It is often associated with monoclonal gammopathy, but does not manifest multiple myeloma. Since Clarkson et al. described the first case in a 34- year-old woman, about 50 cases have been reported in the literature. However, most of the cases were of adult age, and the mean age of onset in the reported cases was 42.6 years. In literature review, we could refer only one pediatric case of SCLC by Foeldvari et al. in 1995. We report another pediatric case of SCLS.

Keyword

Systemic capillary leak syndrome; Child

MeSH Terms

Adult
Age of Onset
Capillaries
Capillary Leak Syndrome*
Child*
Female
Humans
Hypoalbuminemia
Hypotension
Multiple Myeloma
Paraproteinemias