Korean J Med.  2000 Nov;59(5):555-560.

A case of systemic lupus erythematosus with chylothorax, chronic interstitial cystitis and protein-losing enteropathy

• Lee KN
• Park YH
• Lee SH
• Lee JC
• Lim MK
• Cho YS
• You B
• Moon HB

Abstract

Systemic lupus erythematosus(SLE) is the prototypic immune complex disease which involves various organs. Chronic interstitial cystitis and protein-losing enteropathy are uncommon manifestations of SLE and have good response to steroid. Only one case of SLE associated with chronic interstitial cystitis and protein-losing enteropathy has been reported which was resistant to steroid treatment but dramatically responded to cyclophosphamide. We describe a case of a female patient who developed systemic lupus erythematosus associated with chylothorax, interstitial cystitis and protein-losing enteropathy with literature review. This case was initially resistant to steroid but with the addition of cyclophosphamide, chylothorax, chronic interstitial cystitis and protein-losing enteropathy markedly improved. This is the first case of SLE that developed chylothorax as well as chronic interstitial cystitis and protein-losing enteropathy.

Keyword

Lupus erythematosus; Systemic; Cystitis, Interstitial; Protein-losing enteropathy

MeSH Terms

Chylothorax*
Cyclophosphamide
Cystitis, Interstitial*
Female
Humans
Immune Complex Diseases
Lupus Erythematosus, Systemic*
Protein-Losing Enteropathies*
Cyclophosphamide