Korean J Urol.  2004 May;45(5):495-497.

Renal Cell Carcinoma Associated with Von Hippel-Lindau Disease Treated by Wedge Resection

• Kang IS
• Lee YI
• Seo IY
• Jeong HJ
• Rim JS

Abstract

The Von Hippel-Lindau disease is an autosomal dominant condition manifested by the cerebellar hemangioblastomas, retinal angiomas, cysts of the pancreas, the kidney, and the epididymis, pheochromocytoma, and renal cell carcinoma. Renal cell carcinoma occurs in 35% to 38% of affected individuals and may cause pain or a palpable mass. We report a case of a 45-year-old female with renal cell carcinoma, cerebellar hemangioblastoma, and cysts of the pancreas and kidney, to which a wedge resection was performed.

Keyword

Von Hippel-Lindau disease; Renal cell carcinoma

MeSH Terms

Carcinoma, Renal Cell*
Epididymis
Female
Hemangioblastoma
Hemangioma
Humans
Kidney
Male
Middle Aged
Pancreas
Pheochromocytoma
Retinaldehyde
von Hippel-Lindau Disease*
Retinaldehyde