Korean J Pediatr Gastroenterol Nutr.  2008 Sep;11(2):214-218.

Primitive Neuroectodermal Tumor of the Liver in a 13-year-old Boy: A Case Report

• Lee SG
• Kim JE
• Lee JH
• Lee HJ
• Lee JS
• Lee JH
• Choe YH

Abstract

Primary primitive neuroectodermal tumor (PNET) of the liver is a rare disease with aggressive behavior and poor prognosis. We report a case of a PNET of the liver in a 13-year-old boy. The patient was admitted to the hospital with fever and abdominal pain. Abdominal CT and MRI revealed a 5.5 cm sized, septated, non-enhancing mass in the hepatic hilum. The patient was initially diagnosed with an inflammatory pseudotumor. Despite 9 days of antibiotic therapy, the patient's clinical symptoms did not improve. A liver biopsy was performed in the interest of formulating a differential diagnosis. This procedure revealed tumor cells positive for CD99 on immunohistochemistry. The patient was diagnosed with a PNET.

Keyword

Liver; PNET

MeSH Terms

Abdominal Pain
Adolescent
Biopsy
Diagnosis, Differential
Fever
Granuloma, Plasma Cell
Humans
Immunohistochemistry
Liver
Neuroectodermal Tumors, Primitive
Prognosis
Rare Diseases