Ann Dermatol.  2012 Nov;24(4):464-467. 10.5021/ad.2012.24.4.464.

A Wedge-Shaped Anterior Hairline Extension Associated with a Tessier Number 10 Cleft

• Lee HM
• Noh TK
• Yoo HW
• Kim SB
• Won CH
• Chang SE
• Lee MW
• Choi JH
• Moon KC

• KMID: 2266044
• DOI: http://doi.org/10.5021/ad.2012.24.4.464

Abstract

A wedge-shaped anterior hairline extension is a very rare skin manifestation usually associated with congenital anomalies including a Tessier number 10 cleft. Other associated conditions are the Tessier number 9 cleft, the Fraser syndrome, and the Manitoba oculotrichoanal syndrome (MOTA syndrome). The Tessier number 10 cleft features include a coloboma of the middle third of the upper eyelid, and an eyebrow divided into two portions. The medial eyebrow portion may be absent and the lateral portion is angulated vertically, joining the hairline of the scalp. This creates a wedge-shaped anterior hairline extension. Herein we report on a case of a wedge-shaped anterior hairline extension associated with the Tessier number 10 cleft.

Keyword

Anterior hairline extension; MOTA syndrome; Tessier number 10 cleft

MeSH Terms

Abnormalities, Multiple
Anal Canal
Coloboma
Eyebrows
Eyelids
Fraser Syndrome
Hypertelorism
Manitoba
Scalp
Skin Manifestations
Abnormalities, Multiple
Anal Canal
Coloboma
Hypertelorism

Figure

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  Fig. 1 Wedge-shaped anterior hairline extension and scar after surgical repair of a Tessier number 10 cleft (right eyelid).

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  Fig. 2 Terminal hair follicle (H&E, ×40).

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