Korean J Med.
2011 Dec;81(6):775-779.
A Case of Pulmonary Lymphangioleiomyomatosis Associated with Tuberous Sclerosis and Renal Angiomyolipoma
- Affiliations
-
- 1Department of Internal Medicine and Pulmonology and Critical Care, Kyung Hee University School of Medicine, Seoul, Korea. faab01@naver.com
- 2Department of Pulmonology and Critical Care, Kyung Hee University East-West Neo Medical Center, Seoul, Korea.
Abstract
- Tuberous sclerosis is an autosomal dominant disorder characterized by facial skin lesions, epilepsy, and mental retardation. Pulmonary involvement in tuberous sclerosis is rare and shows characteristic reticulonodular infiltration and cystic changes. Lymphangioleiomyomatosis is characterized by the progressive proliferation of smooth muscle cells and occurs in 0.1-1% of patients with tuberous sclerosis. We encountered a case of pulmonary lymphangioleiomyomatosis associated with tuberous sclerosis and bilateral renal angiomyolipoma in a 31-year-old female patient. This case is reported here along with a brief review of the literature.
- Full Text Links
-
- Actions
-
Cited
- CITED
-
- Close
- Share
-
- Similar articles
-
- A Case of pulmonary lymphangioleiomyomatosis developed in tuberous sclerosis with renal angiomyolipoma
- Spontaneous Rupture of Renal Angiomyolipoma in a Female Tuberous Sclerosis Patient with Pulmonary Lymphangioleiomyomatosis
- A Case of Unilateral Renal Angiomyolipoma Associated with Tuberous Sclerosis
- A case of bilateral renal angiomyolipoma associated with tuberous sclerosis
- Concurrent renal and hepatic angiomyolipoma with pulmonary involvement in two patients with tuberous sclerosis
