Korean J Med.  2011 Jun;80(6):712-717.

A Case of Erdheim-Chester Disease Mimicking Systemic Lymphangitic Metastasis

Affiliations
  • 1Department of Internal Medicine, Ewha Womans University School of Medicine, Ewha Medical Research Institute, Seoul, Korea. hs1017@ewha.ac.kr
  • 2Department of Pathology, Ewha Womans University School of Medicine, Ewha Medical Research Institute, Seoul, Korea.

Abstract

Erdheim-Chester disease (ECD) is non-Langerhans cell histiocytosis that leads to multi-organ involvement with unknown etiology. We report a 64-year-old woman with a dry cough and dyspnea. She had interlobular septal thickening and ground-glass opacity in both lungs, suggesting lymphangitic lung metastasis. However, she was diagnosed with ECD after a long bone and immunohistological evaluation.

Keyword

Erdheim-Chester disease; Lung; Retroperitoneal fibrosis

MeSH Terms

Cough
Dyspnea
Erdheim-Chester Disease
Female
Histiocytosis
Humans
Lung
Middle Aged
Neoplasm Metastasis
Retroperitoneal Fibrosis
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