J Korean Soc Radiol.  2015 Feb;72(2):143-146. 10.3348/jksr.2015.72.2.143.

Erdheim-Chester Disease with Perirenal Masses Containing Macroscopic Fat Tissue

Affiliations
  • 1Department of Radiology, St. Vincent's Hospital, College of Medicine, The Catholic University of Korea, Suwon, Korea. bellenina@daum.net

Abstract

Erdheim-Chester disease is a rare non-Langerhans-cell histiocytosis involving multiple organs. On histological evaluation, lipid-laden histiocyte aggregates in Erdheim-Chester disease is detected, but fat tissue in affected organs is not noted grossly on computed tomography. A 40-year-old man presented with bilateral perirenal masses containing fat tissue. He was diagnosed as perirenal involvement of Erdheim-Chester disease. This report describes a case of Erdheim-Chester disease with perirenal involvement that demonstrates unusual features.


MeSH Terms

Adult
Erdheim-Chester Disease*
Histiocytes
Histiocytosis, Non-Langerhans-Cell
Humans
Kidney
Retroperitoneal Fibrosis
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