Korean J Dermatol.  2012 May;50(5):456-459.

Parry-Romberg Syndrome with Band-like Linear Alopecia

• Choi SI
• Yang JH
• Park YL
• Lee JS
• Whang KU
• Lee SH

Abstract

Parry and Romberg described progressive facial hemiatrophy, characterized by progressive unilateral wasting of the skin, fat, muscle and bone in 1825 and 1846, respectively. Involvement of the central nervous system, with impairment of neurologic function, occurs infrequently. Linear scleroderma on frontal and parietal scalp, named 'en coup de sabre', is considered an overlapping condition. An 11 year-old girl was presented to our office with left facial hemiatrophy and transverse linear band-like alopecia on her posterior parietal scalp. Histopathologically, there was a sclerotic change of the collagen fibers and dermal lymphocytic infiltrations around the skin appendages. Her skin lesion has improved by intralesional corticosteroid injection. Linear scleroderma frequently coexists with Parry-Romberg syndrome. But in this case, she had a unique pattern of scleroderma, which is distinct from the previously reported cases.

Keyword

Facial hemiatrophy; Linear scleroderma; Parry-Romberg syndrome

MeSH Terms

Alopecia
Central Nervous System
Collagen
Facial Hemiatrophy
Muscles
Scalp
Scleroderma, Localized
Skin
Collagen