J Korean Neurol Assoc.
2012 May;30(2):141-144.
Parry-Romberg Syndrome with Intermittent Exotropia
- Affiliations
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- 1Department of Neurology, Gyeongsang National University School of Medicine, Gyeongsang National University Hospital, Jinju, Korea.
- 2Department of Neurology, Pusan National University School of Medicine, Pusan National University Yangsan Hospital, Yangsan, Korea. artery1975@naver.com
Abstract
- Parry-Romberg syndrome, or progressive facial hemiatrophy, is a rare and acquired neurocutaneous disease of unknown etiology that is classically characterized by progressive and self=limited atrophy of the skin, subcutaneous tissues, and underlying bone structures. Ophthalmic involvement is reportedly not uncommon, and the most common ocular finding is enophthalmos. Here we report a 46=year=old woman with Parry=Romberg syndrome who presented with intermittent exotropia of the right eye. To the best of our knowledge, this is the first description of intermittent exotropia in a patient with Parry-Romberg syndrome.