J Korean Ophthalmol Soc.  2013 Jun;54(6):958-961. 10.3341/jkos.2013.54.6.958.

A Case of a Congenital Lacrimal Outflow Dysgenesis with Supernumerary Lacrimal Puncta

• Chun JW
• Yang SW

• KMID: 2217274
• DOI: http://doi.org/10.3341/jkos.2013.54.6.958

Abstract

PURPOSE
To report a case of congenital lacrimal outflow dysgenesis with supernumerary lacrimal puncta.
CASE SUMMARY
A 45-years-old woman presented with chronic bilateral epiphora with no specific medical history. Slit-lamp examination revealed bilateral upper and lower double puncta. The accessory puncta were situated along the lid margin, medial to the normal one and had a typical slit configuration. Additionally, there was a lower canalicular system block that appeared unresponsive to simple probing. Bilateral endoscopic conjunctivodacryocystorhinostomy with Jones tube was performed. Chronic bilateral epiphora was relieved after bilateral endoscopic conjunctivodacryocystorhinostomy with Jones tube.
CONCLUSIONS
A case of congenital lacrimal outflow dysgenesis with supernumerary lacrimal puncta was observed, which has not been previously reported in Korea. Surgical repair of the congenital lacrimal outflow dysgenesis with supernumerary lacrimal puncta should be considered to achieve a functional recovery of the lacrimal drainage system.

Keyword

Congenital lacrimal outflow dysgenesis; Supernumerary lacrimal puncta

MeSH Terms

Drainage
Female
Humans
Korea
Lacrimal Apparatus Diseases

Figure

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  Figure 1. Pre-operative photographs of canaliculi obstruction and lacrimal dysgenesis. Lacrimal probe was exposed through canaliculi. (A) Right upper puncta, (B) Left upper puncta, (C) Right lower puncta, (D) Left lower puncta.

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  Figure 2. An axial computed tomography image shows bi-lateral nasolacrimal canal opacification.

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  Figure 3. Post-operative photographs of endoscopic conjunctivodacryocystorhinostomy state. The Lester-Jones’ tubes were inserted bilaterally. (A) Right eye, (B) Left eye.

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