J Korean Radiol Soc.  1999 Sep;41(3):503-506. 10.3348/jkrs.1999.41.3.503.

Imaging Findings of Arteriovenous Malformations Involving Lung and Liver in Hereditary Hemorrhagic Telangiectasia (Osler-Weber- Rendu Disease): Two Cases Report

• Yi JG
• Lee JH
• Seong SO

• KMID: 2200821
• DOI: http://doi.org/10.3348/jkrs.1999.41.3.503

Abstract

Hereditary hemorrhagic telangiectasia (HHT) or Osler-Weber-Rendu disease is an autosomal dominant disorder characterized by repeated episodes of bleeding. Multiple telangiectases consisting of thin-walled, dilated vascular channels with arteriovenous communication may involve, for example, mucocutaneous tissue, the gastrointestinal tract, and the liver, lung, and brain. We report the imaging findings of two cases of HHT involving arteriovenous malformation of both the lungs and liver, a rare condition. Chest radiography revealed a round mass, while helical CT showed a feeding artery and draining vein with arteriovenous malformation in the lung. Color Doppler sonography revealed an enlarged and tortuous hepatic artery with high systolic velocity. CT demonstrated an enlarged hepatic artery, arteriovenous shunt, and early draining hepatic vein in the liver. Celiac angiography showed arteriovenous malformation.

Keyword

Arteriovenous malformations, hepatic; Arteriovenous malformations, pulmonary; Telangiectasia

MeSH Terms

Angiography
Arteries
Arteriovenous Malformations*
Brain
Gastrointestinal Tract
Hemorrhage
Hepatic Artery
Hepatic Veins
Liver*
Lung*
Radiography
Telangiectasia, Hereditary Hemorrhagic*
Telangiectasis
Thorax
Tomography, Spiral Computed
Veins