Ann Dermatol.  2009 Nov;21(4):435-439. 10.5021/ad.2009.21.4.435.

A Case of Erythrodermic Dermatomyositis Associated with Gastric Cancer

• Kim SW
• Kang YS
• Park SH
• Lee UH
• Park HS
• Jang SJ

• KMID: 2156516
• DOI: http://doi.org/10.5021/ad.2009.21.4.435

Abstract

Erythroderma is an unusual cutaneous finding associated with dermatomyositis. There are only five cases of erythrodermic dermatomyositis reported in the English literature. We treated a case of erythrodermic dermatomyositis associated with a Bormann type 1 gastric cancer. The patient had a generalized, erythematous scaly eruption consistent with erythroderma and Gottron's papules as well as a heliotrope rash; these are the hallmark skin manifestations of dermatomyositis.

Keyword

Dermatomyositis; Erythroderma; Gastric cancer; Malignancy

MeSH Terms

Dermatitis, Exfoliative
Dermatomyositis
Humans
Skin Manifestations
Stomach Neoplasms

Figure

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  Fig. 1 Erythematous scaly patches involving more than 90 percent of the total body area.

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  Fig. 2 Hallmark cutaneous skin manifestations of dermatomyositis including (A) heliotrope rash and (B) Gottron's papules were noted.

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  Fig. 3 Histopathology of the skin lesion showed a hyperkeratotic stratum corneum, epidermal atrophy, hydropic degeneration of the basal cell layer, papillary dermal edema, dermal mild perivascular lymphocytic infiltration and increased mucin deposition (H&E, A: ×40, B: ×200).

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